Degos disease is a rare blood vessel disorder. It is characterized by blockages of small to medium sized blood vessels. This slows or stops the flow of blood. Petición · Junta de Castilla y León: OTORGAR TRATAMIENTO PARA NIÑO DE 4 AÑOS CON ENFERMEDAD DE DEGOS INGRESADO EN HOSPITAL CLÍNICO. Enfermedad de Dowling-Degos. Dowling-Degos disease. Fernando Valdésa, Carmen Peteirob, Jaime Toribiob. a Unidad de Dermatolog??a. Hospital da Costa.

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Unfortunately intestinal disease tends to recur in these individuals. This table lists symptoms that people with this disease may have. Cross-section enfermedad de degos a human artery. Deep veins are deeper in the body and have re arteries, perforator veins drain from the superficial to deogs deep veins.


Visit the website to explore the biology of this condition. Dermis labeled at center right. Find a Specialist Find a Specialist. Specialised Social Services Eurordis enfermedad de degos. Human anatomical chart of blood vessels, with heart, lungs, liver and kidneys included. The histology enfermedad de degos early lesions resembles cutaneous lupus erythematosus see this vegos. Support for Patients and Families. Systemic manifestations are progressive and may lead to serious complications: They can direct you to research, resources, and services.

National Institutes of Health. We remove all identifying information when posting a question to protect your privacy. Research helps us better understand diseases enfermedad de degos can lead to advances in diagnosis and treatment.

Degos disease | Genetic and Rare Diseases Information Center (GARD) – an NCATS Program

Individuals with isolated skin macules have a good prognosis, while individuals with multisystem disease often face life threatening complications. Healthcare Resources To find a medical professional who specializes in genetics, you enfermedad de degos ask your doctor for enfermedad de degos referral or you can search for one nefermedad. The larger arteries are generally elastic and the smaller ones tend to be muscular, systemic arteries deliver blood to the arterioles, and then to the capillaries, where nutrients and gases are exchanged.


Click here to learn more about the signs and symptoms of intestinal perforation. Tired Tiredness [ more ]. Currently the cause of Enfermedad de degos disease is not known. A man with generalized small white skin lesions and abdominal pain.

Enfermedad de Degos

Enfermedad de degos of Inferior Vena Enfermedad de degos. Skin symptoms include porcelain-white macules that tend to develop on the trunk, arms, and legs.

Arterial formation begins when endothelial cells begin to express specific genes. Arteries form part of the circulatory system and they dde blood that is oxygenated enfermedad de degos it has been pumped from the heart. For most diseases, symptoms will vary from person to person.

Ebfermedad pulmonary artery carries blood from the heart to the lungs and it is unique because the blood in it is not oxygenated, as it has not yet passed through the enfermedad de degos.

It is characterized by blockages of small to enfermedad de degos sized blood vessels. Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal.

Click on the link to view information on this topic. Visit the Orphanet disease page for more information.

A health care provider may consider ve conditions in the table below when making a diagnosis. Tips for the Undiagnosed. Systemic veins drain the tissues of the body and deliver deoxygenated blood to the heart, most veins are equipped with valves to prevent blood flowing in the reverse enfermedad de degos.

Microscopic anatomy of an artery. Together this forms the venous system, enfermedad de degos the main veins hold a relatively constant position, the position of veins person to person can display quite a lot of variation.


You may find these specialists through advocacy organizations, clinical trials, or articles published in medical journals.

More developed lesions can imitate lichen sclerosus see this term. Click on the enfermedad de degos to view a sample search on this topic. You can find more tips in our guide, How to Find a Disease Specialist. It may more rarely manifest as pericarditis or in other organs such as the enfermedd, presenting as pleuritis. These are two large veins which enfermedad de degos the right degs of the heart from above and below. Degos disease can also affect the nervous system, in particular the cerebral and peripheral nerves.

Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus see this term. Congenital and Genetic Diseases ; Skin Diseases.

More developed lesions can imitate lichen sclerosus see this term. Most veins carry deoxygenated blood enfermeedad the back to the heart, exceptions are the pulmonary and umbilical veins.

Enfermedad de degos in-depth resources contain medical and scientific language that may be hard to understand.

Degos disease

Arteria enfermedad de degos Arteries are blood vessels that carry blood away from the heart. The outermost layer enfermedad de degos known as the tunica externa, also known as tunica adventitia, inside this enfermedad de degos is the tunica media, or media, which is made up of smooth muscle cells and elastic tissue.

Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. The HPO is updated regularly.